The term non-cirrhotic portal hypertension (NCPH) refers to a heterogeneous group of liver disorders that primarily affect the liver vascular system and that are classified anatomically on the basis of site of resistance to blood flow, as pre-hepatic, hepatic (pre-sinusoidal, sinusoidal or post-sinusoidal) and post-hepatic [1, 2].
非肝硬化门脉高压(NCPH)指的是主要影响肝血管系统的异质性肝脏疾病，根据血流阻力部位在解剖学上分为肝前、肝（窦前、窦后或窦后）和肝后[1,2]。
For years they have been considered quite rare conditions, but their scarce frequency was mostly due to the poor knowledge and to the low grade of suspicion.
多年来，它们一直被认为是相当罕见的情况，但它们的罕见频率主要是由于知识不足和怀疑程度较低。
However, in the last years, the multicentric cooperation together with the unification of the several terminologies and nomenclatures used to name these diseases led to deepen the knowledge on the clinical features, presentation and management of vascular liver diseases.
然而，在过去的几年里，多中心合作，以及用于命名这些疾病的几个术语和命名法的统一，导致加深了对血管性肝病的临床特征、表现和管理的认识。
The term PSVD replaced the term INCPH in order to include the patients with specific histological features but no clinical signs portal hypertension.
术语PSVD取代了术语INCPH，以包括具有特定组织学特征但没有临床体征的门静脉高压的患者。
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