哪种是血管畸形？（Which is a vascular malformation？）
Characterization of the vascular malformation
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Truncular VM |
Tissular VM |
Components: artery, lymphatic veins
Abnormalities: length, diameter number pathway
Remnants embryologic vessels
AV fistula … |
Capillary M
Venous M
-Common
-Glomuvenous
Lymphatic M
Arteriovenous M |
Mixed VM
Capillary, venous, lymphatic |
Association with other tissue abnormalities: Klippel trenaunay S, Parkes Weber S, Proteus S, Maffucci S |
那种病变不是血管畸形呢？ （Which lesions are not vascular malformations?）
Which lesions are not vascular malformations?
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Dupplex |
MRI |
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V M |
2-3% |
Present at birth |
Grows commensurably with body growtho |
Venous M:No spontaneous flow
ArteriovenousM: AV shunt |
Diffuse lesion
T1: hypo
T2: Hyper (venous flow)hypo(fast flow)
T1gado:arterial or venous enhancement |
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haemangioma |
1,2% |
Neonatal period |
Rapidly growing Long involution stage |
Tissular mass
Hypo or hyperechogenicity
Hypervascularization
Systolic velocity↑ RI↓ |
Well circumscribed mass
T1:iso
T2: hyper
T1gado: arterial enhancement |
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Infantile haemangioma |
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Present at birth |
Non involutive (NICH)
Involutive (RICH)a |
Tissular mass
Hypo or hyperechogenicity
Hypervascularization
Systolic velocity↑ RI↓ |
Well circumscribed mass
T1:iso
T2: hyper
T1gado: arterial enhancement |
我们最初应该为血管畸形做点什么呢？ Do we Initial work up of the vascular malformation？
制定治疗计划吧 Treatment plan:
–但问题是什么？What is the problem?
- 需要选择那种治疗呢？ Which treatment?
–什么是联合治疗 The multidisciplinary approach
随访 Follow-up
遗传咨询 Genetic counselling
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